Supravalvar aortic stenosis (SVAS) is a form of congenital left ventricular outflow tract (LVOT) obstruction that occurs as a localized or diffuse narrowing of the ascending aorta beyond the superior margin of Course a pied - Femme - Vetements - Cuissard the sinuses of Valsalva.SVAS is a rare progressive congenital heart defect with a higher risk of sudden cardiac death.Our patient was a 30-yearold man M Shoes referred by his GP for an incidental finding of heart murmur.Echocardiography showed a hypertrophic left ventricle with an increased pressure gradient.CT and MRI angiography and eventual arteriography confirmed the diagnosis by showing a narrowing of the aorta at the sinotubular junction with significant accelerated flow.
This stenosis was eventually surgically corrected with no complications.